101 - Adjustable Removable Prosthesis for Primary Dentition in Ectodermal Dysplasia

Ectodermal dysplasia is a rare genetic disorder occurring in 1 in 100,000 live births that can be X-linked, autosomal dominant, or autosomal recessive. This condition causes a malformation in two or more ectodermal derivatives including teeth, hair, nails, and sweat glands, with some individuals also presenting with cleft lip and/or palate. Affected individuals often experience disturbances in tooth development, which may result in oligodontia, hypodontia, defects in tooth eruption, and abnormal variations in tooth size and shape. This case report highlights the fabrication of a removable jackscrew-activated maxillary prosthesis designed to establish function, esthetics, and phonetics in a patient with oligodontia. Additionally, it emphasizes the importance of early intervention as it can significantly impact the emotional and psychological development of patients in school age.

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