306 - Dental Management of Patients With Pierre Robin Sequence

Introduction: Pierre Robin Sequence (PRS) is a congenital condition characterized by a sequence of developmental abnormalities involving head and face. The clinical triad includes micrognathia, glossoptosis, and upper airway obstruction, with or without a cleft palate. Complications include airway obstruction, feeding problems, failure to thrive, recurrent ear infections, etc. Management, depending on severity, varies from nonsurgical to surgical approaches.

Case Report: This presentation discusses the dental management of a 13-year-old boy with PRS. Patient presents with mandibular hypoplasia, sleep apnea, dental anxiety, and is currently undergoing active orthodontic treatment. Patient is not taking any medications and has seasonal allergies. Dental findings include congenital missing permanent teeth, hypoplastic permanent teeth, and caries lesions. Patient is scheduled for a combined ENT/OMFS and full-mouth dental rehabilitation in the operating room.  Restorations under Nitrous Oxide were completed and currently patient is seen every three months for recare appointments.

 

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