388 - Female with Diagnosis of Dandy-Walker Syndrome and Cleft Lip and Palate: a Case Report

Abstract: Dandy-Walker Syndrome (DWS) is a rare congenital brain malformation involving the cerebellum and fourth ventricle, often associated with systemic anomalies. This case report presents a 15-year-old female with DWS, cleft lip and palate, and developmental delays, referred for dental evaluation. Her examination revealed multiple carious lesions, enamel hypoplasia, and poor oral hygiene, influenced by feeding challenges and limited cooperation due to her neurological condition. Comprehensive dental treatment under general anesthesia was required to address her extensive needs.
This case underscores the importance of interdisciplinary care in managing patients with complex medical conditions. Collaboration with her medical and therapeutic team was essential to developing a coordinated treatment plan and providing tailored preventive strategies for her caregivers.
By reviewing dental manifestations and management considerations for patients with DWS and cleft anomalies, this report highlights the critical role of pediatric dentists in improving oral health outcomes in children with rare syndromes.

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